Journal of Current Glaucoma Practice

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VOLUME 7 , ISSUE 2 ( May-August, 2013 ) > List of Articles


An Overlap Syndrome of Pigment Dispersion and Pigmentary Glaucoma accompanied by Marfan Syndrome: Case Report with Literature Review

Tutul Chakravarti, George Spaeth

Keywords : Pigmentary glaucoma, Pigment dispersion syndrome, Marfan syndrome, Ectopia lentis, Intraocular pressure fluctuation, Reverse pupillary block, Exfoliation syndrome

Citation Information : Chakravarti T, Spaeth G. An Overlap Syndrome of Pigment Dispersion and Pigmentary Glaucoma accompanied by Marfan Syndrome: Case Report with Literature Review. J Curr Glaucoma Pract 2013; 7 (2):91-95.

DOI: 10.5005/jp-journals-10008-1143

License: CC BY-NC 4.0

Published Online: 01-12-2018

Copyright Statement:  Copyright © 2013; The Author(s).


‘Overlap syndrome’ describes the situation in which two or more ‘independent’ conditions are present, either one of which could cause a particular finding. This current presentation reports a case with bilateral pigment dispersion syndrome (PDS), advanced pigmentary glaucoma (PG), and the Marfan syndrome, with bilateral subluxation of the lenses, and large short-term and long-term fluctuations of intraocular pressure. It is interesting to consider whether the associated advanced glaucomatous nerve damage could be a manifestation of just the PDS, just the Marfan syndrome, or rather a combination of these two overlapping independent conditions.

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