Citation Information :
Junttila TL, Alberto N, Winkels M, Greenwood MD. Successful Reduction of Intraocular Pressure in a Patient with Glaucoma Secondary to Sturge–Weber Syndrome Using a Suprachoroidal Shunt. J Curr Glaucoma Pract 2020; 14 (1):43-46.
Aim: We present a case of successful reduction of intraocular pressure (IOP) in a patient with Sturge–Weber syndrome (SWS) and moderate open angle glaucoma using a suprachoroidal shunt. Background: Patients with SWS glaucoma often have elevated episcleral venous pressure resulting in elevated IOP. This makes the conventional pathway for aqueous humor outflow a poor target for IOP reduction, yielding it difficult to treat. Medication and procedures that facilitate uveoscleral outflow have been more successful. Case description: We present a case where a suprachoroidal shunt device (CyPass®) was used to reduce IOP in a patient with SWS. The IOP reduction has persisted for 12 months without complication or the requirement for topical prostaglandin analog use. Conclusion: The uveoscleral pathway is a preferred target for IOP reduction in patients with elevated episcleral venous pressure. The CyPass device offers a promising ab interno minimally invasive glaucoma surgery (MIGS) approach to reduce IOP in cases where a pathologic pressure gradient exists in the trabecular meshwork. Clinical significance: Glaucoma in patients with SWS has been historically difficult to treat. Previous surgical procedures that have been successful are more invasive and have required the creation of alternative drainage routes of aqueous humor. The CyPass device offers a promising less invasive option to reduce IOP in these patients.
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