Journal of Current Glaucoma Practice

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VOLUME 9 , ISSUE 3 ( September-December, 2015 ) > List of Articles


Review on the Management of Primary Congenital Glaucoma

Julia Yan Yu Chan, Bonnie NK Choy, Alex LK Ng, Jennifer WH Shum

Keywords : Primary congenital glaucoma, Childhood glaucoma, Goniotomy, Trabeculotomy, Pediatric glaucoma surgery

Citation Information : Yu Chan JY, Choy BN, Ng AL, Shum JW. Review on the Management of Primary Congenital Glaucoma. J Curr Glaucoma Pract 2015; 9 (3):92-99.

DOI: 10.5005/jp-journals-10008-1192

License: CC BY-NC 4.0

Published Online: 01-08-2019

Copyright Statement:  Copyright © 2015; The Author(s).


Despite being documented in medical history from over 2400 years ago, primary congenital glaucoma (PCG), being a disease with low incidence rate, remains a challenge to ophthalmologists. The article provides a broad overview on the pathophysiology and diagnostic approach to PCG with major emphasis on the treatment options of PCG. While reviewing on the well-established treatment options, namely goniotomy, trabeculo-tomy and combined trabeculotomy-trabeculectomy, emphasis has also been made to recent updates on secondary treatments: trabeculectomy, antimetabolites, glaucoma-drainage devices and cyclodestructive procedures. It is, however, important to note that the rarity of PCG places limitations on study design, most studies are, thus, retrospective, nonrandomized and have different definitions of surgical success. Ophthalmologists need to interpret the results with critical thinking and formulate individual treatment plans for each patient.

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